Hemophilia Overview

Front

What is hemophilia?

Back

Hemophilia is a rare inherited bleeding disorder in which the blood does not clot normally.

Front

What are the types of hemophilia?

Back

Hemophilia A (factor VIII deficiency) and Hemophilia B (factor IX deficiency).

Front

What are the classifications of hemophilia based on clotting factor levels?

Back

Mild (5-50% of normal factor), Moderate (1-5% of normal factor), Severe (less than 1% of normal factor).

Front

What are the clinical manifestations of hemophilia?

Back

Hemarthrosis, prolonged bleeding from minor trauma, uncontrolled hemorrhage, epistaxis, GI bleeding, hematuria, ecchymoses, pain, hypovolemic shock, and vertigo.

Front

What is hemarthrosis?

Back

Bleeding into joints, which may lead to chronic pain, joint injury, and deformity.

Front

What are the complications of hemophilia?

Back

Joint damage, viral infection, hematuria, and intracranial hemorrhage.

Front

What is the pathophysiology of hemophilia?

Back

Injury to blood vessels leads to bleeding; lack of clotting factors results in weak platelet plugs and delayed fibrin clots.

Front

What are the nursing diagnoses related to hemophilia?

Back

Ineffective tissue perfusion, activity intolerance, impaired skin integrity, body image disturbance, deficit of knowledge, and risk of fluid volume deficit.

Front

What are some nursing interventions for ineffective tissue perfusion?

Back

Assess the cause of bleeding, monitor skin color and tissue perfusion, administer blood as advised, and reposition the patient regularly.

Front

What health education should be provided to clients with hemophilia?

Back

Avoid vigorous exercise, maintain dental hygiene, recognize signs of internal bleeding, and wear a Medic-Alert bracelet.