4 yo M, Recurrent facial swelling

12 yo M. Fam Hx: Maternal uncle had kidney failure at a young age. BP 155/85 mmHg. Hearing screen: Decreased high-freq hearing bilaterally. UA: 2+ proteinuria, 10 RBCs.

7 yo with patellar dislocation, abnormal knee and hip XRs, and dystrophic nails

4 yo F, critically ill, with a normal anion gap metabolic acidosis

2 yo F, Recent AGE, Now bloody diarrhea , fever, irritability, lethargy, dry membranes, diffuse petechiae, hepatosplenomegaly. Hgb 6, Platelets 44, Creatinine 2.4.

Which of the following is most likely to be identified on additional work-up?

10 day old M, Midline abdominal mass in lower abdomen, weak urinary stream.

15 yo Football player

•Syncopal episode during practice

•Temp 105 F

•BP 75/40

•HR 130 bpm

•Oliguria

•Dark urine

•Dipstick: +Heme

•UA: No RBCs

35 week newborn sent to NICU.

•Apparent absence of abdominal musculature

•Wrinkled and redundant skin covering the abdominal wall

•Bilateral cryptorchidism

12 yo M, Sickle cell, priapism not responding to fluids or pain meds