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WorksheetsPediatrics 2
Total questions: 29
Worksheet time: 15mins
What level of risk (number of times the baseline risk) of anaphylaxis to latex do children with spina bifida have?
50
100
500
1000
What level of lesion is correctly paired with the level of lesion in spina bifida and needed assistive device?
Midthoracic lesion – Reciprocal Gait Orthosis
Upper lumbar lesion – HKAFO
Lower Lumbar lesion – AFO
Sacral lesion – Lofstrand crutches
What percentage of children with spina bifida with high lumbar involvement attain community ambulation?
15%
20%
30%
45%
What is not a common finding on physical exam in Muscular Dystrophy?
Pseudohypertrophy of the calf
Gower’s sign
Pelvic Girdle
Wrist Extensors
In DMD, which muscle group tends to develop weakness first?
Neck flexors
Shoulder
Pelvic Girdle
Wrist Extensors
What is the most common type of CP in premature infants?
Diplegic
Hemiplegic
Dyskinetic
Mixed Type
Which subgroup of spastic CP has the highest incidence of significant disability?
Hemiplegia
Diplegia
Triplegia
Tetraplegia
Which of the following is described as a slow rhythmic movement with tone changes in trunk and extremities, associated with abnormal posturing?
Athetosis
Chorea
Choreoathetoid
Dystonia
North Korea
A child walking without assistive devices but with limitations outdoors or in community is gross motor function classification system (GMFCS) Level
1
2
3
4
5
Which of the following is a positive prognostic factor on a child with CP being able to eventually walk?
Crawl by age 3
Sitting independently by age 2
Persistence of 3 or more primitive reflexes by 18-24 months
Prognosis does not depend on type of CP
What is the most common cause of death in patients with myelodysplasia (congenital disorders with failure of the fetal spinal cord to close)?
Central Respiratory Depression
Vasomotor Changes
Tethered Cord
Cardiac Abnormalities
A myelomeningocele at which of the following levels is associated with loss of sympathetic adrenergic innervation to the bladder?
T10-L2
L2-L5
S1-S4
In myelodysplasia patients, which reflex is associated with a greater chance of bowel continence?
Achilles
Bulbocavernosus
Absent Babinski
Fencer
Which of the following is false regarding Spina Bifida patients?
The highest incidence occurs in the UK, and is lowest in Japan.
The higher the lesion in the spinal cord, the lower the IQ.
Independent self-catheterization can be achieved in 5yo. Easier for boys than girls.
Spinal deformities such as kyphosis and scoliosis are most common in lumbar lesions.
Which type of spina bifida is most strongly associated with an Arnold-Chiari Type 2 malformation?
Spina Bifida Occulta
Meningocele
Myelomeningocele
Myelocele
Which of the following is not a recommended test for juvenile myasthenia?
Repetitive EMG stimulation at 4-10 Hz
Tensilon Test
Single-fiber EMG
Muscle Biopsy
AIDP is least associated with which of the following infectious illnesses
CMV
EBV
Campylobacter
HSV
A child who has a positive Gower's sign, lives to adulthood, and has a mutation on chromosome 5q11-q13 carries which diagnosis
SMA 1
SMA 2
SMA 3
BMD
This is the number 1 cause of mortality in childhood neuromuscular disease
Cardiovascular complications
Pulmonary complications
Seizures
Neglect
This disease is associated with nearly 100% incidence of scoliosis within 10 years and a mitochondrial protein defect
DiGeorge Syndrome
Cri du Chat
Freidreich's Ataxia
Duchenne's Muscular Dystrophy
What is the genetic inheritance pattern of Emery-Dreifuss muscular dystrophy?
Autosomal Dominant
Autosomal Recessive
X-linked
Mitochondrial
Facioscapulohumeral muscular dystrophy is autosomal dominant disorder primarily affecting what muscles?
Facial and Shoulder girdle muscles
Shoulder girdle and hip girdle muscles
Facial and Hip girdle muscles
Shoulder girdle and Plantar flexors
What EMG finding would you expect to find in Myotonia Congenita?
Increased Recruitment pattern
High Amplitude potentials
Myotonic discharges
Fibrillations
In Central Core Myopathy what muscle fibers are predominantly affected?
Type II fibers
Type I fibers
Type 1 and Type 2 equally
All of Tylers muscles fibers
As part of the Individuals with Disabilities Education Act (IDEA) which of the following services are required for individuals under the age of 3 years old with developmental delay?
Physical Therapy
Speech Therapy
Occupational Therapy
Recreational Therapy
Which of the following is also known as neurodevelopmental treatment (NDT) in which the goal is to normalize tone, inhibit abnormal primitive reflex patterns, and facilitate automatic reactions with subsequent normal development?
Bobath Technique
Phelps Technique
Deaver Technique
Rood Technique
Which age is generally preferred for a patient with cerebral palsy to get a selective posterior rhizotomy?
1-3 years old
3-8 years old
8-12 years old
12-16 years old
Which of the following is true about aging with cerebral palsy?
There is no correlation between degree of disability and level of sexual activity.
Scoliosis occurs much more frequently in ambulatory individuals
General health related problems occur at a rate that is twice as often as the general population.
Individuals with CP are often not capable of reproduction
By what age should the asymmetric tonic reflex be suppressed in an infant?
4-5 months
6-7 months
7-8 months
9-10 months
