Vascular Villains

What is the most common primary vascular tumor of the retina?

• Retinoblastoma

• Hemangioblastoma

• Choroidal melanoma

• Retinal cavernous hemangioma

Von Hippel-Lindau disease is associated with which intraocular vascular tumor?

• Choroidal hemangioma

• Retinal capillary hemangioblastoma

• Retinoblastoma

• Uveal melanoma

What is the typical fundoscopic appearance of a retinal capillary hemangioblastoma?

• Large pigmented lesion with drusen

• Bright red-orange vascular lesion with feeder vessels

• White, calcified mass with exudation

• Small yellow lesions with a honeycomb pattern

Sturge-Weber syndrome is associated with which intraocular vascular tumor?

• Retinal hemangioblastoma

• Choroidal hemangioma

• Retinal cavernous hemangioma

• Choroidal melanoma

Von Hippel-Lindau (VHL) disease follows which pattern of inheritance?

• Autosomal recessive

• Autosomal dominant

• X-linked recessive

• Mitochondrial inheritance

Which chromosome is affected in Von Hippel-Lindau (VHL) disease?

• Chromosome 17

• Chromosome 3

• Chromosome 9

• Chromosome 22

What is the characteristic feature of a retinal cavernous hemangioma on fluorescein angiography (FFA)?

• Early hyperfluorescence with leakage

• "Grape-like" clusters with autofluorescence in late phases

• Hypofluorescence with blocked choroidal flow

• Rapid dye washout

Which of the following conditions is NOT associated with the Von Hippel-Lindau gene mutation?

• Retinal hemangioblastoma

• Choroidal melanoma

• Pheochromocytoma

• Renal cell carcinoma

Which laser treatment is commonly used for small retinal capillary hemangioblastomas?

• Argon laser photocoagulation

• Cryotherapy

• Plaque radiotherapy

• Vitrectomy

Which condition often requires a combination of laser photocoagulation and systemic therapy?

• Sporadic retinal hemangioblastoma

• Retinal capillary hemangioblastomas in Von Hippel-Lindau disease

• Choroidal hemangioma

• Retinal cavernous hemangioma