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WorksheetsPractice 4 (PPS)
Total questions: 50
Worksheet time: 25mins
The following are acyanotic congenital heart disease with left to right shunt lesions EXCEPT
ASD
PAPVR
PDA
Coarctation of aorta
The following are acyanotic congenital heart disease with left to right shunt lesions EXCEPT
ASD
PAPVR
PDA
Coarctation of aorta
A 16-year-old female who was diagnosed to have chronic ITP. What additional laboratory test should be required ?
autoimmune screening test such as ANA
bleeding time
platelet aggregation test
coagulation parameter such as PT AND PTT
The laboratory screening test that is affected by a reduced level of Factor VIII or Factor IX is
Clotting time
Bleeding time
Partial thromboplastin time
Prothrombin time
The usual therapeutic dose of elemental iron can increase hemoglobin by
1 g/dl/day to 2 g/dl/day
0. 8mg/dl/day
0.1 mg/dl/day
0.25mg/ dl/day to 0.4mg/dl/day
The most consistent clinical manifestation of pneumonia in children
Cough
Fever
Tachypnea
Cyanosis
Which is TRUE about recurrent UTI?
2 episodes of cystitis
VUR gr 2
2 or more episodes of acute pyelonephritis
all of the above
Physical abuse includes the following except
beating
shaking
burning
pinching
The most important marker of Abusive Head Trauma ( AHT) is
seizure
coma
retinal hemorrhages
lethargy
A 7 month old boy was brought to the ER due to fall from a hammock. There were no other associated symptoms such as fever, cough or colds, with loss of consciousness for 5 secs but no vomiting. PE was unremarkable except for note of retinal hemorrhages extending to the periphery. CT scan was normal. Probable diagnosis:
Traumatic brain injury
Neglect
Shaking
Meningitis
It is the most common fracture in abused infants
Rib and Sternal fractures
Femoral and humeral fractures
Clavicular fracture
Rib, metaphyseal and Skull fractures
Syndrome of inappropriate antidiuretic hormone secretion (SIADH) is characterized by
Extravascular volume expansion
High serum uric acid
High blood urea nitrogen
Euvolemic hyponatremia
Normal anion gap metabolic acidosis can occur in
Diarrhea
Liver failure
Severe anemia
Starvation ketoacidosis
Which of the following is not actively reabsorb in ascending loop of Henle?
Sodium
Water
Chloride
Bicarbonate
Which is true about Fluid therapy for anuric child
Replacement of insensible fluid losses (25-40% of maintenance) with D5 0.45 NSS + KCL; Replace urine output ml/ml with solution based on measured urine electrolytes
Replacement of insensible fluid loss with NSS + 10mEq/L KCL; Replace output ml/mL every 1-6hrs
Replacement of insensible fluid loss with NSS + 20mEq/L KCL; Replace output ml/mL every 1-6hrs
Replacement of insensible fluid losses (25-40% of maintenance) with D5 0.45NSS; Replace urine output with D5 0.45 NSS +KCl
Initial manifestations of genetic metabolic diseases are the following except:
poor feeding
(non GI caused) vomiting
rashes
lethargy
The main organ damaged by PKU is
liver
kidney
brain
heart
A 3 month old infant is admitted to the hospital for lethargy. You note a doll-like face, apparent muscle weakness and hepatomegaly. Laboratory studies are remarkable for hypoglycemia and lactic acidosis. Ketones are present. You are most concerned for which family of diseases:
Mitochondrial disorder
Glycogen Storage Disorder
Fatty Acid Oxidation Disorder
Disorder of Amino Acid Metabolism
The newborn state screen results for a healthy full-term infant reveals elevated methionine
concentrations. Laboratory analysis shows increased serum and urine homocysteine. Confirmatory testing is positive for homocystinuria. The child is at risk for all of the following, EXCEPT:
Downward dislocated lens
Osteoporosis
Short stature
Seizures
A patient presents with pellagra like symptoms and noted impaired intestinal tryptophan transport
Hartnup syndrome
Ornithine Carboxylase deficiency
Argino succinate lyase deficiency
Tyrosinemia
A 3 year old boy was brought due to pallor. On PE there was hyperpigmentation of the trunk, neck and intertriginous areas, café-au-lait spots and with upper limb abnormalities. He was small for his age. What is the most likely diagnosis?
Schwachman-Diamond syndrome
Dyskeratosis congenita
Fanconi anemia
Reticular dysgenesis
What is the expected response to iron therapy in 48-72 hours, What is your diagnosis?
Repletion of iron stores
Reticulocytosis
Increase in hemoglobin level
Erythroid hyperplasia
The best and most cost effective first step treatment of ITP is:Hgb 7.0 gm/dl, WBC 23 (83 % neutrophiles ) Platelet 11 x 10 9/L , Urea 49 mmol/L , Creatinine 437 mmol/L , PT 12 sec ( control 12-13 sec)
What is your diagnosis?
Observe closely and do nothing unless there are complication
Try a brief course of oral prednisone
Anti D as the first step
IVIG treatment
A 7 year old child with a history of 7 days fever with nausea vomiting and diarrhea . Over the past 24 hours he was noted to have developed purpuric spots over the limbs, and have become anemic Lab results are:
Hgb 7.0 gm/dl, WBC 23 (83 % neutrophiles ) Platelet 11 x 10 9/L , Urea 49 mmol/L , Creatinine 437 mmol/L , PT 12 sec ( control 12-13 sec)
What is your diagnosis?
Henoch-Schoenlein Purpura
Hemolytic Uremic Syndrome
Autoimmune thrombocytopenic purpura
Autoimmune hemolytic anemia
The optimal blood component/s therapy to be given to a patient with signs of bleeding, whom you suspect of hemophilia and work up available is a normal PT and prolonged PTT would be
Cryoprecipitate
Fresh whole blood
Packed Red Cell and DDAP
Fresh Frozen Plasma
This is defined as blood pressure (BP) >95th percentile for age, sex and height upto the 95th percentile + 11mmHg or 130-139/80-89 mmHg for adolescents >13yo
Elevated BP
Hypertension
Stage I Hypertension
Stage II Hypertension
The most common hematologic finding in cyanotic heart disease that needs balance between risk of intravascular thrombosis and bleeding diathesis.
Anemia
Polycythemia
Thrombocytosis
Shortened prothrombin time
If the process undermining is incomplete, the right atrioventricular valve may not separate from ventricular myocardium, its possible cause of process
Noonan Syndrome
Ventricular septal defects
Atrioventricular canala defects
Ebstein anomaly
The “mother's kiss” approach has been successful in acute situations such as _________.
Epistaxis
Nasal foreign bodies
Nasal polyps
Septal hematoma
The MOST common complaint in patients with bronchiectasis is
Cough and production of copious purulent sputum
Hemoptysis
Fever
Anorexia
Which among the following has the highest caffeine content?
Sprite
Coke
Pepsi
Mountain Dew
Mother asks your advice regarding back pack
Backpacks are good way to carry all the books to school
Backpacks place a heavy burden to the spine
It should not be more than 10% of the child’s weight
It should be carried on only one shoulder to lessen the back pain
14 year old male, brought to ER due to seizure. On PE, BP 140/100, generalized edema. Labs: anemia, RBC casts in urinalysis, C3 is low, ASO = 300 IU, creatinine normal, renal ultrasound diffuse parenchymal disease. This is a case of post streptococcal glomerulonephritis with:
Congestive heart failure
Cerebral edema
Hypertensive encephalopathy
None of the above
A child height is above 2 of z-score, weight is below -1, whats the interpretation?
Normal height &weight
Normal height & wasted
Tall and normal weight
Tall and underweight
Boy with known contact to a ptb source, (-) PPD, whats the classification?
PTB I
PTB II
PTB III
PTB IV
Which trait segregate within families but do not exhibit a consistent or recognizable inheritance pattern?
Polygenic inheritance
Multifactorial inheritance
Pseudogenetic inheritance
Nontraditional inheritance
True about Down syndrome except:
95% of cases have 3 copies of chromosome 21
Parent who is translocation carrier have a 75% recurrence risk for chromosomally abnormal child
Cases result in errors in meiosis
97% are maternal in origin
Chromosomal trisomy characterized by ocular hypertelorism, microcephaly, malformed ears, microphthalmia, cleft lip often midline, flexed fingers, polydactyly, and cardiac malformation
Trisomy 8
Trisomy 18
Trisomy 21
Trisomy 13
This refers to the observed structural, biochemical, and physiologic characteristics of an individual
Allele
Genotype
Chromosome
Phenotype
This is true of Hereditary Spherocytosis( HS), except:
It is the most common inherited abnormality of the RBC membrane.
There is lesser incidence of hemolysis in the newborn with this disease because hemoglobin F binds strongly to 2,3 diphosphoglycerate.
Children with HS are susceptible to aplastic crises due to parvovirus B19 infection.
HS can result to anemia, leukopenia, and thrombocytopenia.
Increased reticulocytes in the bloodstream indicates the following conditions :
normal bone marrow response to ongoing rbc destruction secondary to hemolysis
active blood loss
rbc sequestration by the spleen
occurs in a short period after initiating iron therapy
all of the above
Possibility of intestinal obstruction should be considered in infants who does not pass meconium by ____hrs.
48-72hrs
24-48hrs
24-36hrs
>72hrs
The shunting done on patients with severe pulmonary stenosis or pulmonary valve atresia
Glenn shunt
Blalock-Taussig
Fontan
Balloon atrial septostomy
None of the above
The most common delivery room emergency for neonates is
severe anemia
shock
failure to initiate and maintain effective respiration
seizure
2 y/o child bitten by stray dog on the neck w/ complete DPT with booster
Rabies Ig and Rabies vaccine
Rabies Ig only
Rabies Vaccine only
Tetanus toxoid
Other disease that will have strawberry tongue?
Scarlet fever
Measles
German measles
Kawasaki disease
feeds self, seeks help when in trouble, kisses
parent with a pucker, identifies 1 or more parts of
the body
12 months old
15 months old
18 months old
24 months old
infants weighing <1000g can lose as much as
7-8 ml/kg/hr
6-7 ml/kg/hr
4-5 ml/kg/hr
2-3 ml/kg/hr
The first visible sign of puberty in girls is:
thelarche
pubarche
menarche
peak height velocity
In which of the following situations can a diagnosis of acute rheumatic fever be made?
(+) ASO titer (+) joint pains, (+) fever
(-) ASO titer (+) chorea’s syndenham
(+) ASO titer, (+) erythema marginatum ↑ ESR
(+) ASO titer, (+) polyarthritis, ↑ CRP
