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WorksheetsExam 3 (Peds) - Neuromuscular/Diabetes
Total questions: 100
Worksheet time: 53mins
Which of the following is NOT a neuromuscular diagnostic tool?
nerve conduction velocity EMG
muscle biopsy
serum creatinine phosphokinase measurement
laparoscopic endoscopy
Fill in the blank: The most common type of cerebral palsy is _________.
Spastic
Ataxic
Dyskinetic
Hypotonic
Which type of cerebral palsy is characterized by slow, wormlike movements of extremities, trunk, face, and tongue?
Spastic
Athetoid/diskinetic
Ataxic
Mixed/dystonic
Which of the following is a symptom of ataxic cerebral palsy?
Drooling speech problems
Rapid repetitive movements
Combination of spastic and athetosis
Presents as hypotonia
Fill in the blank: Mixed/dystonic cerebral palsy is a combination of ________ and ________.
spastic and athetosis
flaccid and ataxia
rigid and tremor
chorea and myoclonus
Which type of cerebral palsy presents as hypotonia most often, and is considered the most common clinical type?
Spastic
Athetoid/diskinetic
Ataxic
Mixed/dystonic
Fill in the blank: Diplegia affects ________ or ________.
both arms or both legs
the heart or lungs
the eyes or ears
the liver or kidneys
In regards to cerebral palsy, what does Triplegia refer to?
2 extremities affected
3 extremities affected
4 extremities affected
1 extremity affected
Which of the following is NOT a characteristic of Quadriparesis/Tetraparesis?
A) Four extremities involved/severe disability
B) Speech and swallowing difficulties
C) Incomplete tongue protrusion
D) Only lower limbs involved
What is the definition of cerebral palsy (CP)?
Progressive motor dysfunction due to brain damage
Non-progressive motor dysfunction due to brain damage
Non-progressive sensory dysfunction due to brain damage
Progressive sensory dysfunction due to brain damage
SATA: Which of the following is affected by CP?
Cognition
Posture
Muscle tone
Sensory perception
Motion
There is routine postnatal screening for cerebral palsy.
True
False
SATA: Which of the following is a possible motor sign of CP?
Floppy tone
Stiff or rigid limbs
Unable to sit without support at age 8 months
Poor head control after age 3 months
Arching back/pushing away
A child unable to sit without support at age 8 months may have which condition?
Cerebral Palsy
Anencephaly
Spina Bifida
Tetanus
SATA: What are common feeding difficulties in patients with cerebral palsy (CP)?
Persistent tongue thrusting
Excessive drooling
Difficulty swallowing liquids , but not solids
All of the above
Frequent gagging or choking with feeds
Fill in the blank: Strategies to decrease _______ deliveries can help reduce the risk of cerebral palsy (CP).
premature
cesarean
term
multiple
Fill in the blank: Avoidance and prevention of prenatal _______ injuries (injuries where the fetal brain is deprived of oxygen for prolonged periods) is important in preventing CP.
anoxic
toxic
mechanical
chemical
hypotonic
Fill in the blank: Orthotic devices are used to support _______ and prevent contractures in CP management.
alignment
strength
movement
vision
Which of the following is a mobility aid for CP patients?
Standers
Seating systems
Wheelchairs
All of the above
What is the purpose of botulinum toxin in the treatment of CP?
Localized spasticity management
Systemic spasticity management
Reduction of lower extremity ataxia
None of the above
Fill in the blank: Deep brain stimulation is used for severe _______ disorders in CP.
movement
alignment
visual
hearing
What percentage of CP patients have normal IQs?
10-20%
30-40%
50-60%
80-90%
Rigid, atonic, and quadriparetic CP patients have the highest incidence of ________ impairment.
profound
mild
single-limb
auditory
Which of the following is a pharmacologic intervention to decrease CP spasticity?
Botox
Haldol
Morphine
Diphenhydramine
Baclofen can be administered orally or via an implanted pump for ________ administration.
intrathecal
subcutaneous
intravenous
intradermal
Which of the following is NOT a pharmacologic intervention to decrease CP spasticity?
Baclofen
Dantrolene sodium
Diazepam
Propofol
Neural tube defects (NTDs) are the largest group of congenital anomalies with ________ inheritance.
multifactorial
autosomal dominant
mitochondrial
X-linked recessive
autosomal recessive
The incidence of neural tube defects is higher in ____.
girls
boys
A decline in NTDs is attributed to the addition of ________ to the diet.
folic acid
vitamin C
calcium
iron
Which neural tube defect is the most serious and incompatible with life?
Spina bifida occulta
Spina bifida cystica
Anencephaly
Hydrocephalus
Spina bifida occulta is ________ visible externally.
not
always
sometimes
clearly
Spina bifida cystica is visible with an external ________ protrusion.
saclike
bony
muscular
cartilaginous
Fill in the blank: Neurologic deficit occurs in varying degrees with _________
myelomeningocele
hydrocephalus
encephalocele
spina bifida occulta
Myelomeningocele most frequently occurs during which period of pregnancy?
First trimester
Second trimester
Third trimester
First month
First two months
What percentage of myelomeningocele cases occur in the lumbar area?
75%
30%
50%
90%
Which anomaly is most frequently associated with myelomeningocele?
Hydrocephalus
Spina bifida occulta
Scoliosis
Clubfoot
Which of the following is NOT an etiology of myelomeningocele?
Genetic predisposition
Maternal radiation
Maternal viral infection
Maternal substance abuse
Maternal malnutrition
Fill in the blank: An obvious physical defect readily apparent on inspection is a clinical manifestation of ___________.
myelomeningocele
spina bifida occulta
meningitis
pruritiis
There is a high prevalence of latex allergy in patients exposed to latex products during surgery and/or numerous bladder catheterizations.
True
False
Kugelberg-Welander Syndrome Type 3 is also known as ________.
juvenile spinal muscular atrophy
Duchenne muscular dystrophy
amyotrophic lateral sclerosis
Friedreich's ataxia
Kugelberg-Welander Syndrome can have a possible onset all the way up until adulthood. However, what is the usual onset period for Kugelberg-Welander Syndrome Type 3?
First year of life
Second year of life
Fifth year of life
Third year of life
Which muscles are weak in Kugelberg-Welander Syndrome Type 3?
Foot and calf muscles
Thigh and hip muscles
Facial and neck muscles
Hand and arm muscles
All patients with Kugelberg-Welander Syndrome Type 3 will eventually learn to walk.
True
False
What is the life expectancy for individuals with Kugelberg-Welander Syndrome Type 3?
Shortened
Normal
Unknown
Severely reduced
SATA: Guillain-Barre Syndrome (GBS) is characterized by symmetrical paralysis that causes problems with which of the following?
Respiration
Talking
Swallowing
Vision
Hearing
In Guillain-Barre Syndrome, paralysis begins in the ______ extremities and ______ bilaterally.
lower, ascends
upper, descends
distal, descends
proximal, ascends
Guillain-Barre Syndrome has some associations to swine flu immunizations.
True
False
Guillain-Barre Syndrome is frequently preceded by a mild _____ or intestinal infection.
respiratory
cardiac
hepatic
renal
Which of the following best describes the progression of Guillain-Barre Syndrome?
Begins as weakness, progresses to ataxia, then bilateral paresthesia, and finally paralysis
Begins as ataxia, progresses to weakness, then bilateral paresthesia, and finally paralysis
Begins as weakness, progresses to ataxia, then bilateral paralysis, and finally paresthesia
Begins as ataxia, progresses to weakness, then bilateral paralysis, and finally paresthesia
What is the main cause of death in Guillain-Barre Syndrome?
Heart failure
Respiratory failure
Kidney failure
Liver failure
Tetanus is also known as ________.
lockjaw
measles
chickenpox
mumps
Which of the following is NOT a manifestation of tetanus?
Irritability, tonic spasms
Headache, difficulty swallowing, sore throat
Lack of sweat, lethargy, loss of reflexes
Facial spasms: fixed smile, elevated eyebrows
Fever, chills, restlessness
SATA: What are some treatments that the RN can administer to a child AFTER they have been exposed to and contracted tetanus?
tetanus antitoxin
tetanus immune globulin
pancuronium
antibiotics
muscle relaxants
Fill in the blank: Food poisoning resulting from ingestion of toxin produced by the anaerobic bacillus ________ causes botulism.
Clostridium botulinum
Escherichia coli
Staphylococcus aureus
Salmonella typhi
SATA: What are the sources of botulism in infants?
Honey
Unpasteurized milk
Raw eggs
Contaminated water
Corn syrup
What is a common source of botulism in older children?
Fresh fruits
Improperly sterilized home-canned foods
Pasteurized cheese
Bottled honey
SATA: Symptoms of botulism include:
double or blurry vision
slurred speech
difficulty swallowing
dry mouth
muscle weakness
Which of the following is NOT a symptom of botulism?
Slurred speech
Difficulty swallowing
Dry mouth
High fever
Muscle weakness in botulism starts in the ________ and then ________ through the body.
shoulders, descends
legs, ascends
hands, spreads
feet, radiates
CNS symptoms of botulism appear abruptly _____ hours after ingestion of Clostridium botulinum.
12-36
12-24
24-48
48-72
Which of the following is a general sign of botulism?
Weakness
Dizziness
Headache
All of the above
What is often the presenting symptom of botulism?
Constipation
Fever
Blurry vision
Muscle weakness
Dysphagia
Which medications are used to treat botulism?
BabyBIG, trivalent equine antitoxin and bivalent antitoxin
isoniazid and rifampin
acyclovir and ribavirin
None of the above
Autonomic Dysreflexia is also known as spinal cord injury at ______ or higher.
T6
T12
L1
C7
What are some causes of autonomic dysreflexia?
Full bladder, UTI, fecal impaction
Low blood sugar, dehydration, hyperventilation
Asthma, allergic rhinitis, eczema
Migraine, tension headache, sinusitis
Which of the following is NOT a symptom of vasodilation ABOVE the level of injury?
Severely increased BP
Flushed face and headache
Distended neck veins
Pale, cool skin
In autonomic dysreflexia, ______ occurs above the level of the injury, and ______ occurs below the level of the injury.
hemodilution, hemostasis
constipation, incontinence
vasodilation, vasoconstriction
hypotension, hypertension
What is the largest group of muscular diseases in children?
Muscular dystrophies
Myasthenia gravis
Cerebral palsies
Congenital myopathies
All muscular dystrophies have genetic origin with gradual degeneration of muscle fibers, progressive weakness, and wasting of skeletal muscles.
True
False
What is the most severe and most common muscular dystrophy in childhood?
Duchenne Muscular Dystrophy (DMD)
Becker Muscular Dystrophy (BMD)
Facioscapulohumeral Muscular Dystrophy (FSHD)
Limb-Girdle Muscular Dystrophy (LGMD)
Duchenne Muscular Dystrophy (DMD) is also known as ________.
pseudohypertrophic muscular dystrophy
myasthenia gravis
Becker muscular dystrophy
polymyositis
Which of the following is NOT a characteristic of Duchenne Muscular Dystrophy (DMD)?
Onset between 3-5 years
Progressive muscle weakness, wasting, and contractures
Calf muscles hypertrophy in most patients
Y-linked inheritance pattern
Fill in the blank: Duchenne Muscular Dystrophy (DMD) is suspected based on ________.
clinical appearance
blood pressure measurement
hearing test
vision screening
Fill in the blank: Confirmation of DMD is done by EMG, muscle biopsy, and ________ measurement.
serum enzyme
blood pressure
urine glucose
CSF protein
In a child with DMD, serum CPK and AST levels are high in the first 2 years of life, before onset of weakness. Levels ________ as muscle deterioration continues.
diminish
increase
remain unchanged
fluctuate
SATA: Which of the following are clinical manifestations of DMD?
Waddling gait
Gower's sign
Pelvic girdle instability
Saclike protrusion
Overflow incontinence
Fill in the blank: In DMD, ________ is a common spinal abnormality.
lordosis
scoliosis
kyphosis
spina bifida
Fill in the blank: DMD is characterized by enlarged muscles, especially ________ and upper arms.
thighs
calves
shoulders
chest
Fill in the blank: Profound muscular ________ occurs in later stages of DMD.
atrophy
hypertrophy
spasm
regeneration
Steroids are used to reduce inflammation in DMD. What is another type of drug therapy used for DMD?
Gene therapy
Mineralocorticoid replacement therapy
Antiviral and antifungal therapy
DMARD therapy
Chorea is a symptom of diskinetic cerebral palsy and manifests as _____, involuntary movements that worsen with ____ stress.
jerky, emotional
wormlike, physical
tonic-clonic, cardiac
ataxic, psychological
A child is born with anencephaly. What should the L&D RN do next?
Prepare the child for immediate craniotomy
Provide pediatric cardiopulmonary resuscitation
Provide comfort care for the infant
Prepare the child for immediate skull reconstructive surgery
Which is more severe, and actually has a portion of the neural tube inside the saclike protrusion?
meningocele
myelomeningocele
hydrocephaly
spina bifida oculta
SATA: Besides the saclike protrusion, what are some other clinical manifestations of myelomeningocele?
overflow incontinence
urine dribbling
poor anal sphincter tone
orthopedic deformities
respiratory complications
The most dangerous complication of botulism is progressive and life threatening _______ paralysis.
respiratory
cardiac
gastrointestinal
upper extremity
SATA: What are some clinical manifestations of botulism in INFANTS?
loss of head control
feeding difficulty
weak cry
diminished gag reflex
hypotonia
The life expectancy for a child with DMD is _____ years.
less than 40 years
less than 10 years
less than 20 years
less than 5 years
SATA: What are the hallmark "3 Ps" of diabetes?
Polyuria
Proteinuria
Polydipsia
Pruritis
Polyphagia
A child with diabetes has a(n) ______ risk of infection.
increased
decreased
SATA: Select of the criteria for diabetic ketoacidosis.
BG level over 200 mg/dL
Blood pH lower than 7.3
Blood pH higher than 7.6
Serum bicarbonate level lower than 15 mEq/L
Positive anion gap
What are Kussmal's respirations?
hyperventilation to eliminate excess CO2
hypoventilation to eliminate excess CO2
hyperventilation to acquire more CO2
hypoventilation to acquire more CO2
What is the FIRST thing the RN should prepare to do when treating a child presenting with DKA?
check blood glucose
administer insulin
draw CBC and BMP
begin fluid resuscitation
The initial volume expansion treatment for children with DKA is _______ ml/kg of an isotonic solution (NS or LR) over the first hour.
20-40
10-20
5-10
40-80
A continuous insulin drip for a pediatric DKA patient should be set to:
10 U/kg/hr
1 U/kg/hr
0.1 U/kg/hr
0.01 U/kg/hr
A child is on an insulin drip for DKA. How much should their BG level drop per HOUR?
50-100 mg/dL
100-200 mg/dL
5-10 mg/dL
200-500 mg/dL
A child is receiving treatment for DKA. What should the RN be MOST concerned about with this child?
hypoglycemia
hypokalemia
cerebral edema
pitting edema
hyponatremia
SATA: If a hypoglycemic child can drink and swallow, the Rule of 15 should be used to boost their BG. If a hypoglycemic child CANNOT swallow, what should the RN do?
50% dextrose IVP based on age
50% dextrose IVP based on weight
1 mg glucagon IM
1 mg glucagon SQ
1 mg glucagon IVP
A child with diabetes is presenting to the ED with signs of acute illness. How often should their urine be checked for the presence of ketones?
every hour
every 3 hours
every 6 hours
every 12 hours
Insulin glargine (Lantus) peaks at 30-90 minutes after administration.
True
False
A RN used the Rule of 15 to bring a child's blood sugar above 70 mg/dL. Now that this target level is reached, what should the RN do next?
give child another simple carbohydrate
give child a complex carbohydrate
administer insulin as ordered
administer 50% dextrose IVP as ordered
